Multiple Plexiform Xanthomatous Tumor: A Rare Occurrence in A Young Girl

Abstract

Kanthilatha Pai, Poornima Baliga, Ramachandra Lingadakai, Sathish Pai

Plexiform Xanthomatous Tumor (PXT) is a rare benign tumor occurring in the dermis and subcutis composed of xanthomatous cells arranged in a distinct plexiform pattern. This condition has been found to occur exclusively in males. A rare occurrence of multiple plexiform xanthomatous tumors in a young female clinically diagnosed as multiple neurofibromatoses is presented. Literature search revealed only one case of PXT reported in female. Hence this case is presented for its rarity.